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A Case of Sturge-Weber Syndrome

Published online by Cambridge University Press:  29 January 2018

Winifred M. Small
Affiliation:
Dingleton Hospital, Melrose

Extract

In 1879 Sturge described a patient with hemiparesis, epilepsy and a facial naevus. He ascribed the neurological condition to a naevus of the brain similar to that on the patient's face. Weber gained the distinction of providing the other half of the eponym by describing the radiological appearances of a similar case. In 1955, however, he advanced the self-effacing descriptive term “encephalofacial angiomatosis”. The essential pathological features of the disorder are facial naevus and leptomeningeal angiomatosis. It is generally agreed that buphthalmos (present in Sturge's original case) is not a necessary component.

Type
Research Article
Copyright
Copyright © Royal College of Psychiatrists, 1963 

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References

Alexander, G. L., and Norman, R. M. The Sturge-Weber Syndrome, 1960. Bristol.Google Scholar
Looney, W. B., Amer. J. Roentgen., 1960, 83, 163.Google Scholar
Sturge, W. A., Trans. Clin. Soc. London, 1879, 12, 162.Google Scholar
Weber, F. P., Brit. Med. J., 1955, i, 726.Google Scholar
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